> Avoid rejuvenation surgery for patients with Ehlers-Danlos syndrome and progeria because of wound healing issues.
> Cutis laxa and pseudoxanthoma elasticum are the only congenital skin disorders that are responsive to surgical rejuvenation.
## EHLERS-DANLOS SYNDROME (CUTIS HYPERELASTICA)
- Incidence: 1:5,000
- Variable inheritance patterns
- Connective tissue disorder, collagen cross-linking problem
- Hypermobile joints
- Thin, friable, hyperextensive skin predisposing patients to
- **Poor wound healing**, hypertrophic scarring
- Redundant periocular skin (e.g., epicanthal folds, wide nasal bridge)
- Ventral hernia
## PROGERIA (HUTCHINSON-GILFORD SYNDROME)
- Incidence: 1:1,000,000
- Autosomal recessive
- Skin laxity, loss of subcutaneous fat
- **Poor wound healing**
- Growth retardation, premature death
- Craniosynostosis, micrognathia
- Baldness, prominent ears
- Findings similar to premature aging
## WERNER’S SYNDROME (ADULT PROGERIA)
- Rare, autosomal recessive disorder
- Features of premature aging
- Scleroderma-like skin
- Hyperpigmentation and hypopigmentation of skin
- **Microangiopathy (contraindication to plastic surgery)**
- Diabetes, cataracts
- High-pitched voice, baldness
## CUTIS L AXA (ELASTOLYSIS)
- Incidence: Only several hundred cases known worldwide
- Variable inheritance patterns, can also be acquired
- Hypoelastic (degeneration of elastic fibers in the dermis), does not spring back immediately when stretched (hyperextensible)
- Appearance of premature aging
- **Wound healing normal**
- Other associated problems
- ↗ risk of ventral hernia
- Cardiopulmonary and gastrointestinal issues
## PSEUDOXANTHOMA ELASTICUM
- Incidence: 1:25,000–100,000
- Variable inheritance patterns
- Skin laxity from calcification and degeneration/fragmentation of elastic fibers
- Cobblestone yellowish plaques characteristic
- **Wound healing normal**
- Ocular and cardiac manifestations
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